Cystic Fibrosis

Cystic Fibrosis is autosomal recessive, lack of protein to transport chloride leading to excessive absorption of water and sodium leading to thick viscous mucous.The risk of it is genetic.The diagnostic exam is Sweat Chloride Test.The cardinal signs are delayed G& D, frequent respiratory infection,Right CHF, Vitamin K deficiency.The drug of choice is Dornase to hydrolyze the DNA in the sputum.The primary concern is hydration.